[1]毛翎羽,周文明,熊梦燎,等.皮肤僵硬综合征1例并文献复习[J].中国皮肤性病学杂志,2019,(10):1164-1167.[doi:10.13735/j.cjdv.1001-7089.201812016]
 MAO Lingyu,ZHOU Wenming,XIONG Mengliao,et al.A Case of Stiff Skin Syndrome and Literature Review[J].The Chinese Journal of Dermatovenereology,2019,(10):1164-1167.[doi:10.13735/j.cjdv.1001-7089.201812016]
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皮肤僵硬综合征1例并文献复习
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《中国皮肤性病学杂志》[ISSN:1001-7089/CN:61-1197/R]

卷:
期数:
2019年10期
页码:
1164-1167
栏目:
病例报告
出版日期:
2019-09-13

文章信息/Info

Title:
A Case of Stiff Skin Syndrome and Literature Review
文章编号:
1001-7089(2019)10-1164-04
作者:
毛翎羽周文明熊梦燎段晓倩
安徽医科大学第一附属医院皮肤性病科,安徽医科大学皮肤病研究所,安徽 合肥 230032
Author(s):
MAO LingyuZHOU WenmingXIONG MengliaoDUAN Xiaoqian
(Department of Dermatology,the First Affiliated Hospital of Anhui Medical University,Institute of Dermatology,Anhui Medical University,Hefei 230032,China)
关键词:
皮肤僵硬综合征 临床特征 组织病理
Keywords:
Stiff skin syndrome Clinical features Histopathologic features
分类号:
R 758.6
DOI:
10.13735/j.cjdv.1001-7089.201812016
文献标志码:
B
摘要:
患儿男,13岁。2岁时发现右股内侧的皮肤僵硬伴凹陷,5岁时发现右腰部的皮肤僵硬伴凹陷,僵硬部位的皮肤毳毛增多、增粗。皮损组织病理示:真皮层未见明显炎症细胞浸润,深层胶原纤维组织增生增粗,胶原纤维组织间可见脂肪组织。诊断:皮肤僵硬综合征(SSS)。
Abstract:
A 13-year-old boy was first noted with stony hard skin on the medial site of the right thigh at two years old.At the age of five,the skin of the right waist was stiff and depressed with excess and thick vellus hairs on the stiff skin.Histological examination showed no inflammatory infiltration in the dermis.Thickening and proliferation of collagen fibers were observed in the lower dermis.Adipose tissue was present between collagen fibers.The diagnosis of stiff skin syndrome(SSS)was made.

参考文献/References:

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备注/Memo

备注/Memo:
[作者单位] 安徽医科大学第一附属医院皮肤性病科,安徽医科大学皮肤病研究所,安徽 合肥 230032
[通讯作者] 周文明,E-mail:aydzwm@163.com
更新日期/Last Update: 2019-09-12